FEATURES

FAMILY

DESCRIPTION

Also known as LIPT2_HUMAN, LIPT2. Catalyzes the transfer of endogenously produced octanoic acid from octanoyl-acyl-carrier-protein onto the lipoyl domains of lipoate-dependent enzymes, which catalyze essential redox reactions (PubMed:28757203). Lipoyl-ACP can also act as a substrate although octanoyl-ACP is likely to be the physiological substrate (By similarity).

EXTERNAL LINKS

uniprot
enzyme classification
PhosphoSitePlus

LIPT2

Putative lipoyltransferase 2, mitochondrial

Mutations

Mutation(s) distribution

Mutations table

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