FEATURES

FAMILY

DESCRIPTION

Also known as NDUV1_BOVIN, NDUFV1, UQOR1. Core subunit of the mitochondrial membrane respiratory chain NADH dehydrogenase (Complex I) which catalyzes electron transfer from NADH through the respiratory chain, using ubiquinone as an electron acceptor. Core subunit of respiratory chain NADH dehydrogenase (Complex I) which is composed of 45 different subunits (PubMed:10852722, PubMed:18721790). This is a component of the flavoprotein-sulfur (FP) fragment of the enzyme (PubMed:10852722, PubMed:18721790). Interacts with RAB5IF (By similarity).

EXTERNAL LINKS

uniprot
enzyme classification

NDUFV1

NADH dehydrogenase [ubiquinone] flavoprotein 1, mitochondrial

Mutations

Mutation(s) distribution

Mutations table

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