FEATURES

FAMILY

DESCRIPTION

Also known as SQOR_HUMAN, SQOR, SQRDL. Catalyzes the oxidation of hydrogen sulfide with the help of a quinone, such as ubiquinone-10, giving rise to thiosulfate and ultimately to sulfane (molecular sulfur) atoms. Requires an additional electron acceptor; can use sulfite, sulfide or cyanide (in vitro) (PubMed:22852582). It is believed the in vivo electron acceptor is glutathione (PubMed:25225291, PubMed:29715001).

EXTERNAL LINKS

uniprot
enzyme classification
PhosphoSitePlus

SQOR

Sulfide:quinone oxidoreductase, mitochondrial

Mutations

Mutation(s) distribution

Mutations table

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