FEATURES

FAMILY

DESCRIPTION

Also known as COQ9_HUMAN, COQ9, C16orf49. Lipid-binding protein involved in the biosynthesis of coenzyme Q, also named ubiquinone, an essential lipid-soluble electron transporter for aerobic cellular respiration. Binds a phospholipid of at least 10 carbons in each acyl group. May be required to present its bound-lipid to COQ7. Homodimer. Interacts with COQ7.

EXTERNAL LINKS

uniprot
enzyme classification
PhosphoSitePlus

COQ9

Ubiquinone biosynthesis protein COQ9, mitochondrial

Mutations

Mutation(s) distribution

Mutations table

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